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Case Studies | Ophthalmology | India | Volume 10 Issue 6, June 2021
A Case Report on Kearns Sayre Syndrome: A Rare Oculomyoencephalopathy
Abhishikta Chakraborty | Utkarsh Rai  | Jawahar Jyoti Kuli 
Abstract: A 22 year short-statured female presented with progressive drooping of both upper eyelids, gradually progressive restriction of eye movements in all gazes. No complaint of diplopia or diminution of vision, no diurnal variation; no history of prior ocular surgery or trauma. She complained of generalised weakness and mild hearing loss. BCVA was 6/6 OU. Chin & Brow elevation present, B/L mild ptosis with preserved Bell?s phenomenon. B/L EOM movement limited in all gazes. Direct & consensual reflexes normal. B/L pigmentary retinopathy was present. Audiometry showed B/L sensorineural deafness. ECG showed AV conduction delay with LVH. Multidisciplinary management for ptosis correction, vision & hearing aids was given.
Keywords: KSS, Ptosis, Hearing loss, conductive hearing loss, Sensorineural Hearing Loss, cardiac abnormalities, red ragged fibers, EOM restriction, skeletal muscle biopsy
Edition: Volume 10 Issue 6, June 2021,
Pages: 269 - 271
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Research Paper, Ophthalmology, India, Volume 10 Issue 11, November 2021Pages: 1149 - 1154
Comparison of Retinal Nerve Fibre Layer Thickness in Diabetic Patients with and without Diabetic Retinopathy Using OCT (Optical Coherence Tomography)
Anil Kumar Bhupally  | Raghu V  | Sindu Sulekha Chigiri  | Sidhartha A
Case Studies, Ophthalmology, India, Volume 11 Issue 3, March 2022Pages: 1140 - 1143
A Rare Case of Ocular Myasthenia Presenting with Uniocular Ptosis in a Patient Attending OPD of a Tertiary Care Centre in North Eastern India
Sauvik Barua | Rajendra Nath Gogoi