Newer Approach in Management of OHVIRA Syndrome (Variant of Mullerian Duct Anomaly)

Dr Pallavi Patil, Dr. Shrinivas Gadappa, Dr. Anurag Sonawne

Abstract: This case report details the surgical management of a 14-year-old girl diagnosed with Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA) syndrome - a rare congenital anomaly often misdiagnosed due to its overlapping symptoms with common abdominal conditions like appendicitis. In my view, what stands out most is the successful integration of endoscopic trans-illumination during exploratory laparotomy, allowing for clear delineation and precise resection of the transverse vaginal septum. The patient initially presented with acute urinary retention and lower abdominal pain, symptoms that intensified due to hematocolpos secondary to the obstructed hemivagina. Despite the rarity of OHVIRA, it is evident that early detection using a combination of ultrasound and MRI remains vital, particularly in adolescent females with renal anomalies and menstrual irregularities. This case emphasizes the utility of a single-stage surgical approach, combining effective drainage and anatomical restoration, which not only alleviated symptoms but also preserved future reproductive potential. Taking this further, the report reinforces the growing importance of multidisciplinary coordination and imaging-led decision-making in managing M?llerian duct anomalies. It also reflects the nuanced evolution of surgical interventions from historically invasive methods to more refined, targeted techniques aimed at minimizing long-term complications such as infertility and endometriosis.

Keywords: OHVIRA syndrome, hematocolpos, transverse vaginal septum, M?llerian anomaly, adolescent gynecology

How to Cite?: Dr Pallavi Patil, Dr. Shrinivas Gadappa, Dr. Anurag Sonawne, "Newer Approach in Management of OHVIRA Syndrome (Variant of Mullerian Duct Anomaly)", Volume 14 Issue 8, August 2025, International Journal of Science and Research (IJSR), Pages: 238-241, https://www.ijsr.net/getabstract.php?paperid=MR25730205533, DOI: https://dx.doi.org/10.21275/MR25730205533