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Case Studies | Paediatrics | India | Volume 10 Issue 7, July 2021

Type 1 CPAM as Persistent Respiratory Distress and Failure to Thrive in Neonates: A Case Report

Belekar Neelam | Phirke Deepa

Abstract: Congenital pulmonary airway malformation (CPAM), also known as congenital cystic adenomatoid malformation (CCAM) although rare congenital birth defect but is the most common type of lung abnormality, that includes a dysplastic mass of abnormal lung tissue, consisting of cysts lined by bronchial or cuboidal epithelium, with intervening normal lung tissue. In CPAM an entire lobe of lung is replaced by a non working cystic lesion. It develops as a result of cessation of lung development during various stages of embryogenesis. Originating from different part of bronchial tree. We present a case of the full-term baby presenting as birth asphyxia, having persistent respiratory distress since birth with not gaining weight diagnosed to have type 1 CPAM in postnatal life successfully managed with left lower lobe lobectomy with post-operative resolution of respiratory distress and successful weight gain. They were multicystic lesions with maximum size of 2.5?1.7cm. histologically showing cysts lined by columnar epithelium surrounded by foetal alveoli and areas of fibrosis and inflammatory infiltrate

Keywords: Type 1 Congenital Pulmonary Airway Malformation, Failure to thrive, Respiratory distress, Lobectomy

Edition: Volume 10 Issue 7, July 2021,

Pages: 631 - 634