Anaesthesia Implications in Neurofibromatosis Case for Emergency Cesarian Section

Dr. Aarti Zanwar, Dr. Jyoti Magar

Abstract: Neurofibromatosis type 1 is a rare neurocutaneous condition that can have widespread and deleterious effects on various organ systems, including the spine with implications for the choice of anesthetic technique. Neurofibromas are the characteristic lesions of the condition and not only occur in the neuraxis but may also be found in the oropharnyx and larynx; these may produce difficulties with laryngoscopy and tracheal intubation. We report the case of a parturient, who was received in the emergency room of the maternity ward of our hospital during the active phase of labor, without neuraxial imaging, in whom a cesarean section was indicated and performed under general anesthesia. Anesthesia for the parturient with neurofibromatosis is still not well documented, its management needs to be multidisciplinary, with a careful pre-conception planning.

Keywords: Neurofibromatosis, Anaesthesia