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India | Medicine Science | Volume 3 Issue 5, May 2014 | Pages: 447 - 449
The Mayer-Rokitansky-K'ster-Hauser (MRKH) Syndrome Associated with Anorectal Malformation ? Rectovaginal Fistula; A Rare Combination: Case Report
Abstract: The Mayer-Rokitansky-Kster-Hauser (MRKH) syndrome is characterized by either isolated uterovaginal agenesis or associated with other organ anomalies in genetic women with normal development of secondary sexual characteristics. It affects at least 1 out of 4500 Women. We report an uncommonly seen unique sub type of MRKH syndrome; co-existing with imperforate anus and rectovaginal fistula (RVF) in a 13 year old adolescent girl presented with passage of stool through introitus. We have discussed in brief the management including vaginal reconstructive surgery and detailed counseling regarding the potentials of coitus and fertility issues
Keywords: Anorectal malformation, Mullarian agenesis, Mayer-Rokitansky- Kster -Hauser syndrome, Rectovaginal fistula, Vaginal agenesis
How to Cite?: Shivaprakash Sosale. C, C. S. Ravikiran, R. Sujatha, "The Mayer-Rokitansky-K'ster-Hauser (MRKH) Syndrome Associated with Anorectal Malformation ? Rectovaginal Fistula; A Rare Combination: Case Report", Volume 3 Issue 5, May 2014, International Journal of Science and Research (IJSR), Pages: 447-449, https://www.ijsr.net/getabstract.php?paperid=20131763, DOI: https://dx.doi.org/10.21275/20131763