Secondary Open-Angle Glaucoma in Sturge-Weber Syndrome - A Case Report

Dr. Aishwarya Kumari, Dr Anuradha A, Dr Nishat Sultana Khayoom

Abstract: Sturge-Weber Syndrome (SWS) is a rare neurocutaneous disorder characterized by facial capillary malformations, leptomeningeal angiomatosis, and ocular abnormalities, notably glaucoma. This case report describes a 16-year-old female who presented with progressive, painless vision loss in the left eye and a port-wine stain on the left side of her face. Ocular examination revealed episcleral vessel dilatation, elevated intraocular pressure (38 mm Hg), and glaucomatous optic nerve changes in the left eye, consistent with secondary open-angle glaucoma associated with SWS. Despite maximal medical therapy, intraocular pressure remained uncontrolled, and a trabeculectomy was performed, resulting in effective pressure reduction over a two-month follow-up period. This case underscores the importance of early recognition and multidisciplinary management of glaucoma in SWS to prevent irreversible vision loss and highlights the ocular clues that may point toward this neurocutaneous diagnosis.

Keywords: Sturge-Weber Syndrome, neurocutaneous, port wine stain, glaucoma, trabeculectomy

How to Cite?: Dr. Aishwarya Kumari, Dr Anuradha A, Dr Nishat Sultana Khayoom, "Secondary Open-Angle Glaucoma in Sturge-Weber Syndrome - A Case Report", Volume 14 Issue 7, July 2025, International Journal of Science and Research (IJSR), Pages: 305-310, https://www.ijsr.net/getabstract.php?paperid=SR25702090901, DOI: https://dx.doi.org/10.21275/SR25702090901