Prosthodontic Management of a Young Patient with X-Linked Hypohidrotic Ectodermal Dysplasia, A Case Report

Nadeem Nasir Kanaan, Nader Naif Al Rawabdeh, Fadi Kamel Obeidat, Abdullah Mohammad Alhawari, Abeer Abed alaziz Al Rawabdeh

Abstract: Hypohidrotic ectodermal dysplasia is a group of malformative disorders characterized by the lack or failure of development of ectodermal derivative organs, including skin, mouth lining, anus, nostrils, sweat glands, hair, nails, and teeth. The impact on teeth may range from oligodontia to the more severe forms of anodontia, leading to significant psychological and functional challenges for the patient. As dentists, our role is crucial in replacing their missing teeth. Dental treatment options vary based on factors such as the patient's age, the number and shape of present teeth, and dentoalveolar growth. The case was for a 15-year patient with hypohidrotic ectodermal dysplasia treated with upper removable partial and lower complete dentures because of extremely missing teeth and the low quality and quantity of bone available achieving good esthetic and functional results.

Keywords: Anodontia, oligodontia, hypohidrotic ectodermal dysplasia, removable appliance