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Case Studies | Health and Medical Sciences | Volume 11 Issue 4, April 2022 | Pages: 25 - 27 | Morocco
Multiple Stromal Tumors in Von Recklinghausen Disease: A Real Diagnostic and Therapeutic Challenge
Abstract: Gastrointestinal stromal tumours (GIST) are rare. They usually occur sporadically, or may be part of a pathological framework such as Neurofibromatosis type 1, and Carney's triad. Familial forms exist. GISTs associated with Neurofibromatosis Type 1 differ from sporadic GISTs in terms of epidemiology, clinical, immunohistochemical, molecular biology, prognosis, and therapeutic management. We report the case of a patient with multiple GISTs in relation to Neurofibromatosis type 1, with the aim of outlining the diagnostic and therapeutic difficulties through a review of the literature.
Keywords: Gastrointestinal stromal tumours, Von Recklinghausen disease, therapeutic challenge
How to Cite?: Nacir Oussama, Ait Errami Adil, Oubaha Sofia, Samlani Zouhour, Krati Khadija, "Multiple Stromal Tumors in Von Recklinghausen Disease: A Real Diagnostic and Therapeutic Challenge", Volume 11 Issue 4, April 2022, International Journal of Science and Research (IJSR), Pages: 25-27, https://www.ijsr.net/getabstract.php?paperid=SR22326004220, DOI: https://dx.doi.org/10.21275/SR22326004220