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Informative Article | Ophthalmology | India | Volume 10 Issue 1, January 2021

A Case of Bilateral Hereditary Optic Neuropathy in a Patient of Progressive Atypical Multiple Sclerosis (Infantile / Behrs Optic Atrophy): A Rare Case Report with Literature Review

Dr. Vimal J. Vyas ^[5] | Dr. Ashish Pandey ^[4]

Abstract: We report a rare case of Bilateral infantile/Behr’s hereditary optic atrophy in a young male patient who came with neurological complaints and blurring of vision. Examination and investigations revealed patient having progressive atypical Multiple sclerosis complicating with optic atrophy. Patient’s neurological symptoms were treated and he was explained about the poor visual prognosis. Behr’s optic atrophy presents with optic atrophy associated with multiple neurological conditions like ataxia, mental retardation, increased tonicity, urinary incontinence

Keywords: Behr's optic atrophy, Mendelian inheritance, Atypical Multiple sclerosis, poor visual prognosis

Edition: Volume 10 Issue 1, January 2021,

Pages: 851 - 853