Isolated Left Ventricular Noncompaction in a 25 Year Old Male

Albert T Pochury, Patrick R Marak, Johan Vanlalpeka

Abstract: Ventricular noncompaction (VNC) of the myocardium is a rare genetic cardiomyopathy caused by a disorder during endocardial morphogenesis and could be accompanied by life-threatening complications. The major clinical manifestations of VNC are heart failure, arrhythmias, and embolic events. The left ventricle is the most commonly reported affected site, but a few cases of right ventricular involvement have also been reported. We report the case of a young male who presented with features of heart failure. Trans thoracic echocardiography showed the characteristic trabeculations of left ventricular noncompaction with associated depressed left ventricular dysfunction.

Keywords: ventricular noncompaction, spongiform cardiomyopathy