Hearing Loss in Leukodystrophy

Thenmozhi K, Pauline Gracia R V, Reenu Celshiya A

Abstract: Aim This study aims to emphasize the role of audiologist in audiological diagnosing and providing audiological rehabilitative management for person identified with Leukodystrophy. Design A single case study Method Audiological assessment is done using Pure Tone Audiometry, Immitance Audiometry, Oto-Acoustic Emissions, Auditory Brainstem Response. Result The child is identified to have almost all features of Leukodystrophy such as severe to profound hearing loss, delay in speech and language development, walking difficulties resulting from spasticity.

Keywords: Leukodystrophy, Myelin sheath, Central Nervous System