L G Akpo, N Badji, H Deme, A D Diop, N M Sy, M Ly, M H Toure, F G Niang, I Niang, M Diouf, K. Diouf, et E H Niang
Abstract: We report three cases of Marfan disease, all of the same siblings, aged from 22 years, 29 years and 39 years, referred to our department for a thoracic and cerebral angioscan. Examinations were conducted with a 64-bar Siemens CT scanner with a dual-body automatic injector from Medrad. Various thoracic complications found featured: aneurysm of the ascending thoracic aorta and apical subpleural blebs. Stanford Type A aortic dissection was noted in two cases. A mild bilateral pneumothorax was found in one patient. To the brain assessment, only one patient presented aneurysm of left carotid siphon. Angioscan remains the reference exam for the assessment of cardio-vascular monotoring during Marfan disease. It allows identify serious complications such as thoracic aorta aneurysms that engages the vital prognosis.
Keywords: Marfan disease, aneurysm aneurism, aortic dissection