Hematemesis as Initial Presentation of Non - Cirrhoticportal Hypertension

Dr. Navtej Singh, Dr. Tarun, Dr. Arvind

Abstract: Idiopathic non-cirrhotic portal hypertension (INCPH) is a rare disease characterized by intrahepatic portal hypertension in the absence of cirrhosis, other causes of liver disease and splanchnic venous thrombosis. We report a case of a18-year-old female who presented to us with a history of pain abdomen from 7 days, fever and generalized weakness from 4-5 days, black coloured stools from 2 days and one-episode of hematemesis on the day of admission. All known causes of hypersplenism were ruled out and she was diagnosed to have idiopathic massive splenomegaly with portal hypertension and hypersplenism.

Keywords: Hematemesis, Non-cirrhotic Portal hypertension, Hypersplenism, Ascitis, Oesophageal varices, Pancytopenia