A Case Report on Generalised Hailey - Hailey Disease (HHD): Inherited Acantholytic Disorder

Dr. Nikhat, Suwaiba Zakir Hussain, Syed Abu Hassan

Abstract: Benign chronic familial pemphigus (Hailey - Hailey disease) is a rare autosomal dominant blistering skin disorder characterised by acantholysis of the epidermis. The classical symptoms are manifested as an eruption of vesicles and bullae with multiple crusted erythematous, excoriated erosions and macerated plaques. We report a 40 - year - old female presenting with similar lesions at flexural folds regions over the intertriginous areas on neck folds, axillary folds, antecubital fossa, inframammary folds, and gluteal folds of varying sizes and photosensitivity. The patient was successfully treated with oral antimicrobials, oral steroids, topical steroids, emollients, and multivitamins.

Keywords: Hailey Disease, HHD, Inherited Acantholytic Disorder

How to Cite?: Dr. Nikhat, Suwaiba Zakir Hussain, Syed Abu Hassan, "A Case Report on Generalised Hailey - Hailey Disease (HHD): Inherited Acantholytic Disorder", Volume 12 Issue 8, August 2023, International Journal of Science and Research (IJSR), Pages: 1129-1132, https://www.ijsr.net/getabstract.php?paperid=MR23812211143, DOI: https://dx.doi.org/10.21275/MR23812211143