Isolated Pulmonary Hypertension with Anti-SS-A/Ro Antibodies Positivity - A Rare Case

Dr. Ashwin Pund, Dr. Swapnil Sapre

Abstract: Pulmonary Hypertension is an entity with varied types of causes. Multiple studies have also suggested an autoimmune component to the development of Pulmonary Hypertension. [1] Here is a described case of a patient with Pulmonary Hypertension and positive antinuclear antibodies (ANA) with high anti-SSA/Ro titers without associated Sj?gren's Syndrome. Anti-SSA/Ro antibodies have been described in pulmonary disease in the literature, but rarely in pulmonary hypertension. This case is a rare presentation of Pulmonary Hypertension presenting with symptoms of right heart failure in conjunction with otherwise asymptomatic Sj?gren's syndrome with elevated ANA and anti-SSA/Ro antibodies.

Keywords: Isolated Pulmonary Hypertension, Anti-SS-A/Ro Antibodies