Congenital Lobar Emphysema

Varundev Sirpuram, Milind Joshi Sir

Abstract: Background: Congenital Lobar Emphysema (CLE), Congenital lobar emphysema (CLE) is a rare malformation of lung development which may be the cause of respiratory insufficiency of the suckling child. It is caused by the hyper inflation of the lung lobe with compression of the normal lung parenchyma and contra lateral displacement of the mediastinum. Over distension and hyperinflation of the pulmonary lobe is secondary to partial bronchial obstruction. Most common affected lobe are upper lobe followed by middle lobe but any lobe may be affected. There is inspiratory air entry but collapse of the narrow bronchial lumen during expiration. The bronchial defect results in lobar air trapping.

Keywords: congenital lobar emphysema, CLE atelectasis, hyperinflation, lobectomy, case report