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Case Studies | Surgery | India | Volume 12 Issue 10, October 2023
Rapunzel Syndrome: A Rare Presentation with Multiple Small Intestinal Bands and Perforation
Dr. Shubham Chobey | Dr. Bharti Sarawat | Dr. Lalit Kishor | Dr. Mahendra [19]
Abstract: Introduction: Rapunzel syndrome was 1st reported in literature by Vaughan et al in 1968.Rapunzel Syndrome is an extremely rare intestinal condition resulting from ingestion of hair (trichophagia) extending from stomach to small intestine. Case Report: We present a case report of 16 year old female with complain of pain abdomen,vomiting and epigastric mass. UGI Endoscopy suggestive of Gastric Trichobezoars.Patient underwent laparotomy gaint trichobejoar with jejunal perforation for which jejunojejunal anastomosis done. Patient discharged with full recovery. Discussion: Rapunzel syndrome occurs predominantly in young women with psychiatry disorder and consist of presence of rare type oftrichobejoar.Trichotillomania and trichophagia were only reported after noticing bald patches on scalp resulting from pulling out and swallowing of hairs.CECT abdomen reveals extend of trichobezoar and gold standard is upper GI endoscopy.Treatment of trichobezoar includeremoval by endoscopy,gastrotomy or enterotomy and laparoscopic etc. Conclusion: CECT and endoscopy is investigation of choice Laparotomy is considered excellent treatment option. Psychiatric assessment and long term follow up advised as a regular part of treatment to prevent recurrence.
Keywords: Rapunzel syndrome, Trichobezoars, Laparotomy, Upper GI endoscopy, CECT abdomen
Edition: Volume 12 Issue 10, October 2023,
Pages: 1999 - 2001