A Rare Case of Pulmonary Lymphangioleiomyomatosis with Recurrent Pneumothorax

Dr. Nalin Shah, Dr. Nirav Lukhi, Dr. Kandarp Nimavat, Dr. Rajdeep Dhandhukiya

Abstract: Lymphangioleiomyomatosis (LAM) is a multisystem disorder, predominantly affecting women. It is characterized by cystic lung lesions, abdominal angiomyolipomas (AML) and lymphatic abnormalities. Our patient was admitted with dyspnea, anorexia, left side chest pain and history of recurrent pneumothorax. She was evaluated with HRCT Thorax & Bronchoscopic biopsy for histopathology and immunohistochemistry. She was diagnosed LAM. She was started on Oral Medroxyprogesterone acetate.

Keywords: Lymphangioleiomyomatosis, cystic lung disease, tuberous sclerosis