Irma Kusumawati, Melita Sylvyana, Endang Sjamsudin
Abstract: Introduction: Juvenile ossifying fibroma (JOF) is a rare benign fibro-osseous lesion in younger children. It has behaviour locally aggressive growth that differentiates from conventional ossifying fibroma (OF). Based on histopathology, JOF is divided into: juvenile psammomatoid ossifying fibroma (JPOF) and juvenile trabecular ossifying fibroma (JTOF). Case Report: A 6-years old girl patient complained of painless progressive swelling at the maxilla and mandible region since she was 4-years old. Excisional biopsy has been performed six times due to the recurrence since 5 years old. The patient is scheduled to periodically followed up to the age of 21 years until definitive therapy can be carried out. Discussion: Diagnosis of JPOF was made based on clinical feature, radiological characteristics, and pathological features. The site of the lesions, involvement of the surrounding vital tissue, patient age, growth rate and parental choice are the factors that must be considered by a surgeon when choosing the right therapy. Conclusion: JPOF lesions presented rapid growth and high rates of recurrence. Surgeon must educate families of JOF patient about tumor characteristics including relapse status, growth rate, treatment plan and the need for periodic follow up to improve the quality of life for JOF patients.
Keywords: aggressive growth, juvenile ossifying fibroma, recurrence rate