Dr. Ajay Vaid, Dr. Amar Singh Thakur, Dr. Mohit Bajaj
Abstract: Tufted angioma and kaposiform hemangioendothelioma are rare vascular tumours that typically occurduring infancy or early childhood. Kasabach-Merritt syndrome is characterised by the combination of rapidly growing vascular tumour, life threatening thrombocytopenia, microangiopathic haemolytic anaemia and consumptive coagulopathy. The blood clotting disorder results from platelets and other clotting factors of the blood being used up within the tumor. Here we report a newborn presenting with swelling left side of neck with bluish tinge on day 1 of life.
Keywords: Kasabach-Merritt syndrome KMS, Hemangioma, Thrombocytopenia, Hypofibrinogenemia