Kocher-Debry Semelaigne Syndrome: An Infrequent Encounter in Hypothyroidism - A Report of Two Cases

Fouziya Sultana | Akshay Wanvat | Shruti Dhale

Abstract: Kocher-Debre-Semelaigne syndrome (KDSS) is a rare association of muscular pseudohypertrophy and long-standing moderate-to-severe hypothyroidism in the paediatric age group. The striking clinical features, availability of a simple treatment and a good prognosis for the condition makes it worthwhile to report such two cases so that all practitioners be aware of the condition and its management.

Keywords: Hypothyroidism, KDSS, Kocher Debre Semelaigne syndrome, Pseudo muscular hypertrophy, Short stature

Edition: Volume 10 Issue 6, June 2021,

Pages: 231 - 234