Downloads: 3
Case Studies | Medical Surgical | Saudi Arabia | Volume 10 Issue 4, April 2021
Place of Tracheotomy in Management of Air Way Obstruction for a Child with Hunter Syndrome Case Report
Dr Madi Sihem, Dr Zoheir Kermezli
Mucopolysaccharidoses (MPS) are composed of inherited conditions coupled with errant mucopolysaccharide degradation. In connective tissues, since these substances are ubiquitous, the manifestations are large and challenging. Deficiencies in the lysosomal enzyme underlie the inadequate degradation of mucopolysaccharides and result in the accumulation in connective tissues of incompletely catabolized substances. There are 11 known deficiencies of enzymes that generate seven recognized MPS phenotypes. It has defined subtypes.11 In patients with type mucopolysaccharidosis (MPS), progressive multi-level upper airway obstruction can develop. Tracheostomy remains an effective technique to protect the airway where other procedures have failed or when the airway obstruction requires several locations, considering the particular challenges posed by these complex patients. The presence of airways is primarily responsible for the substantial anesthetic risk seen in MPS.
Keywords: Tracheostomy, Airway, Mucopolysaccharidoses, Hunter's syndrome, enzyme deficiencies
Edition: Volume 10 Issue 4, April 2021
Pages: 1222 - 1223
How to Cite this Article?
Dr Madi Sihem, Dr Zoheir Kermezli, "Place of Tracheotomy in Management of Air Way Obstruction for a Child with Hunter Syndrome Case Report", International Journal of Science and Research (IJSR), https://www.ijsr.net/search_index_results_paperid.php?id=SR21423140707, Volume 10 Issue 4, April 2021, 1222 - 1223
Similar Articles with Keyword 'Tracheostomy'
Downloads: 1
Case Studies, Medical Surgical, Saudi Arabia, Volume 10 Issue 5, May 2021
Pages: 12 - 14Fractured Tracheostomy Tubes into the Tracheobronchial Tree
Dr. Sihem Madi, Dr Zoheir Kermezli
Downloads: 102
Case Studies, Medical Surgical, India, Volume 8 Issue 11, November 2019
Pages: 1333 - 1335Awake Blind Nasal Intubation as an Alternative to Fibreoptic Intubation
Dr Y V Pratap Kumar, Dr K Sudheer Kumar, Dr A Ramakrishna Rao, Dr A. Venkateswara Rao
Similar Articles with Keyword 'Airway'
Downloads: 1
Case Studies, Medical Surgical, Saudi Arabia, Volume 10 Issue 5, May 2021
Pages: 12 - 14Fractured Tracheostomy Tubes into the Tracheobronchial Tree
Dr. Sihem Madi, Dr Zoheir Kermezli
Downloads: 1
Case Studies, Medical Surgical, Saudi Arabia, Volume 10 Issue 5, May 2021
Pages: 234 - 235The Significance of Early Diagnosis and Clinical Suspicion in a Case of Bronchial Aspiration
Dr. Sihemmadi, Dr. Zoheirkermezli