International Journal of Science and Research (IJSR)

International Journal of Science and Research (IJSR)
Call for Papers | Open Access | Double Blind Reviewed

ISSN: 2319-7064


Downloads: 107

Research Paper | Medicine Science | India | Volume 3 Issue 9, September 2014


Dysencephalia Splanchnocystica

Dr. Muruganantham Balagurunathan [2] | Dr. Ramesh Samikannu | Dr. Ramanathan Ramanathan [2]


Abstract: Dysencephalia Splanchnocystica also called as Meckel-Gruber syndrome is an autosomal recessive disorder1. It is characterized by a traid of occipital encephalocele, large polycystic kidneys, and postaxial polydactyly2. The major diagnostic criteria of MGS include at least 2 of these 3 classic manifestations, occipital encephalocele, cystic renal dysplasia, and polydactyly found in 90 %, 100 % and 83.3 % respectively 3. It is a rare syndrome with highest incidence in Gujarati Indians and Finnish population. We are reporting a case of Dysencephalia Splanchnocystica in a non Gujarati Indian from a municipal town, Sirkazhi in Nagapattinam district in Tamil Nadu, India.


Keywords: Dysencephalia Splanchnocystica, Occipital encephalomeningocele, Postaxial polydactyly


Edition: Volume 3 Issue 9, September 2014,


Pages: 2301 - 2302


How to Download this Article?

You Need to Register Your Email Address Before You Can Download the Article PDF


How to Cite this Article?

Dr. Muruganantham Balagurunathan, Dr. Ramesh Samikannu, Dr. Ramanathan Ramanathan, "Dysencephalia Splanchnocystica", International Journal of Science and Research (IJSR), Volume 3 Issue 9, September 2014, pp. 2301-2302, https://www.ijsr.net/get_abstract.php?paper_id=SEP14628

Similar Articles with Keyword 'Occipital'

Downloads: 134

Case Studies, Medicine Science, India, Volume 6 Issue 8, August 2017

Pages: 1602 - 1603

An Interesting Case of Occipital Neuralgia

Dr Desai VK | Dr Singh VP

Share this Article

Downloads: 148

Informative Article, Medicine Science, India, Volume 7 Issue 1, January 2018

Pages: 860 - 861

Sudden Onset Severe Headache in a Patient of Aplastic Anaemia Following Bone Marrow Transplantation: A Case Report

Krittibus Samui

Share this Article
Top