International Journal of Science and Research (IJSR)

International Journal of Science and Research (IJSR)
Call for Papers | Open Access | Double Blind Reviewed

ISSN: 2319-7064

Downloads: 116

Case Studies | Medicine Science | Albania | Volume 5 Issue 4, April 2016

Merrf Syndrome and Refractory Status Epilepticus

Ilirjana Bakalli [2] | Vahe Mokini

Abstract: MERRF syndrome (or Myoclonic Epilepsy with Ragged Red Fibers) is a mitochondrial disease maternally-inherited. In this progressive disorder, status epilepticus is common and highly resistant to treatment including generalized anesthesia. We report two cases with Merrf syndrome (sister and brother), presented with status epilepticus refractory even to Thiopental, Propofol and Midazolam. In the same family is and another girl, diagnosed with Merrf syndrome. Given that it wasnt possible to stop the refractory status in these cases, we suggest Ketamine as an alternative to general anesthesia as for blocking seizure activity, as for the potential neuroprotective effect.

Keywords: Merrf syndrome, status epilepticus, ketamine

Edition: Volume 5 Issue 4, April 2016,

Pages: 492 - 493

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How to Cite this Article?

Ilirjana Bakalli, Vahe Mokini, "Merrf Syndrome and Refractory Status Epilepticus", International Journal of Science and Research (IJSR), Volume 5 Issue 4, April 2016, pp. 492-493,

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