International Journal of Science and Research (IJSR)

International Journal of Science and Research (IJSR)
Since Year 2012 | Open Access | Fully Refereed | Peer Reviewed

ISSN: 2319-7064




Downloads: 128

Case Studies | Neuroscience | Indonesia | Volume 7 Issue 6, June 2018


Type I Sturge-Weber Syndrome with Bilateral Megalocornea in a Three Years Old Girl

Dewi Sutriani Mahalini [5] | Kadek Surya Jayanti


Abstract: Sturge-Weber syndrome (SWS) is a sporadic condition characterized by presence of port wine vascular nevus (PWS) on the upper part of the face and ipsilateral leptomeningeal angioma. The incidence estimated at 1/50, 000 persons. Common symptoms are seizures, hemiparesis, vascular headache, developmental delay, glaucoma, and hemianopsia. We reported a three years old girl with type I SWS. She had PWS on right side of her face, leptomeningeal angiomatosis, and suspected secondary glaucoma with bilateral megalocornea. She was hospitalized because of seizures and developed transient hemiparesis. CT scan and MRI revealed abnormal calcification on asymmetric right fronto-temporo-parietal area, leptomeningeal angiomatoses and multiple small cavernous hemangioma on the tip of anterior corn of the bilateral lateral ventricle and right thalamus. EEG revealed mild general hypofunction. Patient was treated with carbamazepine and consulted to Ophthalmology, Dermatology, and Neurosurgery Departments but there were no surgery treatment at that time. Long term management was needed to prevent continuing brain damage and complications.


Keywords: Sturge-Weber syndrome, children, bilateral megalocornea


Edition: Volume 7 Issue 6, June 2018,


Pages: 539 - 543


How to Cite this Article?

Dewi Sutriani Mahalini, Kadek Surya Jayanti, "Type I Sturge-Weber Syndrome with Bilateral Megalocornea in a Three Years Old Girl", International Journal of Science and Research (IJSR), Volume 7 Issue 6, June 2018, pp. 539-543, https://www.ijsr.net/get_abstract.php?paper_id=ART20183228

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